Amniogenic band syndrome (ring constriction; streeter dysplasia)

General: Caused by fetus swallowing one or more of the free-floating 626e48g strands that result from amniotic rupture; the tension of these strands intraorally and extraorally produces secondary tears and deformations; no hereditary factor known.

Ocular: Upward slant of palpebral fissures; bilateral upper and lower lid colobomas; telecanthus; bilateral corneal opacities; microphthalmos; strabismus; hypertelorism; epibulbar choristoma; unilateral chorioretinal defects or lacuna (rare).

Clinical: Craniofacial and limb abnormalities.

Braude LL, et al. Ocular abnormalities in the anmiogenic band syndrome. Br J Ophthalmol 1981; 65:299-303.

Hashemi K, et al. Chorioretinal lacuna in the anmiotic band syndrome. J Pediatr Ophthalmol Strabismus 1991; 28: 238-239.

Miller MT, et al. Amniotic bands as a cause of ocular anomalies. Am J Ophthalmol 1987; 104:270-279.

Murata T, et al. A case of anmiotic band syndrome with bilateral epibulbar choristoma. Br J Ophthalmol 1992; 76: 685-687.

Streeter GL. Focal deficiencies in fetal tissues and their relation to intrauterine amputation. Contrib Embryol Carney Inst 1930; 22:1-44.