Kaposi disease (kaposi sarcoma; kaposi hemorrhagic sarcoma; multiple idiopathic hemorrhagic sarcoma; kaposi varicelliform eruption)

General: Vascular tumor of unknown cause; seen most often in males, Jews, and those from eastern Europe, the southern Mediterranean, and Africa; human immunodeficiency virus-related Kaposi syndrome is the most common type of cancer seen in acquired immunodeficiency syndrome patients.

Ocular: Ocular adnexa, varicelliform eruption, including lids, conjunctivae, lacrimal glands, and orbit, may be involved; hemorrhage; extensive injection and thickening of conjunctival tissues; conjunctival involvement more evident in bulbar conjunctiva.

Clinical: Vascular sarcomas usually occur on the legs, although widespread cutaneous and visceral tumors may develop; secondary malignancies are very common; lymphedema.

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