Pityriasis rubra pilaris (kaposi disease [2]; devergie disease; hebra disease; tarral-besnier disease; lichen ruber; lichen ruber acuminatus; pityriasis pilaris) 9

General: Abnormal keratinization of unknown etiology; hereditary and acquired forms have been described in the literature; hereditary form tends to be less severe and more limited in extent.

Ocular: Papules on bulbar conjunctiva; keratitis; ectropion; pannus; corneal ulceration.

Clinical: Cutaneous manifestations; erythema; follicular papules.

Beamer JE, et al. Pityriasis rubra pilaris. Cutis 1972; 10:419-442.

Gilgor RS, et al. Evaluation of 13-cis retinoic acid in lamellar ichthyosis, pityriasis rubra pilaris and Darier's disease. Cutis 1980; 25:380-381,385.

Harley RD. ed. Pediatric Ophthalmology, 4th ed. Philadelphia: WB Saunders, 1998.

McKusick VA. Mendelian Inheritance in Man; A Catalog of Human Genes and Genetic Disorders, 12^th ed. Baltimore: The Johns Hopkins University Press, 1998.

Online Mendelian Inheritance in Man, OMIM. McKusick-Nathans Institute for Genetic Medicine, Johns Hopkins University and National Center for Biotechnology Information, National Library of Medicine, February 12, 2007. World Wide Web URL: https://www.ncbi.nlm.nih.gov/omim/.